Official websites use. Share sensitive information only on official, secure websites. Congenital cystic adenomatoid malformation CCAM is a congenital pulmonary cystic disease that is mostly detected and diagnosed prenatally or during the neonatal period, while rarely being observed in adults.
Here, we report an adult case of CCAM that was diagnosed following surgery for a recurrent pneumothorax. We further review 60 case reports on adult CCAM that have been previously published.
The patient was a year-old woman with a severe left pneumothorax. Her computed tomography scan showed the presence of multiple pulmonary cysts at the base of the left lower lobe. Since she had experienced a left pneumothorax twice previously, surgery was indicated. A wedge lung resection of the pulmonary cysts was performed thoracoscopically. From the review, 7 adult CCAM patients Moreover, malignancies were associated in 8 cases We propose that if multicystic lung lesions are found in pneumothorax patients, particularly in lower lobes, CCAM should be considered during the differential diagnosis, even in adults.
Congenital cystic adenomatoid malformation CCAM is a congenital pulmonary cystic disease in which the adenomatoid proliferation of the bronchiolar epithelium results in the formation of multiple cysts in the lung's lobes.
Most CCAMs are detected and diagnosed prenatally or during the neonatal period when patients present with dyspnea and cyanosis. CCAMs are also sometimes detected in infants and school-age children following respiratory infections, but they are rarely found in adults. We report an adult case of CCAM that was diagnosed following the patient's admission for surgery for a recurrent pneumothorax, and we present a review of 60 case reports on adult CCAM that have been published in the international literature.
